Unilateral Kayser-Fleischer ring.
نویسندگان
چکیده
A patient is presented who had unrecognised Wilson's disease. He had developed a clinically obvious Kayser-Fleischer ring in only one eye. The eye without the corneal ring had been injured in childhood and had a low intraocular pressure. Possible mechanisms for formation of a Kayser-Fleischer ring are reviewed and the lack of Kayser-Fleischer ring in this case is discussed.
منابع مشابه
Kayser-Fleischer ring. A pathological study.
Although the brownish area at the corneal periphery in the region ofDescemet's membrane was first described by Kayser (I902), and Fleischer (I9I2) recognized it as a part of Wilson's disease (hepato-lenticular degeneration), there have been no previous reports in the ophthalmic literature of the United Kingdom of a pathological study of the lesion which is now recognized as a pathognomonic find...
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Here we describe a case of a 22-year-old woman who presented with acute liver failure and Kayser-Fleischer rings suggesting the diagnosis of Wilson's disease.
متن کاملAdvantages of Anterior Segment Optical Coherence Tomography Evaluation of the Kayser-Fleischer Ring in Wilson Disease.
PURPOSE To present anterior segment optical coherence tomography (AS-OCT) findings of the Kayser-Fleischer (KF) ring in Wilson disease (WD) and to discuss the potential advantages of evaluating the KF ring by AS-OCT. METHODS This is a retrospective case series of 7 patients with WD with KF rings seen in our institute during the study period (August 2015 to June 2016). All patients underwent s...
متن کاملEvaluation of Kayser–Fleischer ring in Wilson disease by anterior segment optical coherence tomography
PURPOSE The purpose of the study is to present anterior segment optical coherence tomography (AS-OCT) as an alternative method of evaluating Kayser-Fleischer (KF) ring in Wilson disease (WD) not only by ophthalmologists but also by other clinicians dealing with WD. MATERIALS AND METHODS This was a retrospective case series of six WD patients with KF ring. Evaluation of KF ring was done by nak...
متن کاملWilson's Disease with Neurological Presentation, without Hepatic Involvement in Two Siblings.
Wilson's Disease (WD) is a rare, autosomal, recessive, inborn error of the copper metabolism, which is caused by a mutation in the copper-transporting gene, ATP7B. The presentation is usually neurologic or hepatic, which is seen in 40% of the patients. The diagnosis depends primarily on the clinical features, the biochemical parameters and the presence of the Kayser - Fleischer ring. Here, we a...
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ورودعنوان ژورنال:
- The British journal of ophthalmology
دوره 70 6 شماره
صفحات -
تاریخ انتشار 1986